Thursday, 17 August 2017

Henoch- Schonlein Purpura

Most common vasculitis in children ?

Acute Kidney injury + abdominal pain + palpable purpura = ?

Child with sore throat, runny nose, cough   → 1 week later → muscle aches , red purple rash over arms, buttocks and legs →one month later → fatigue and hematuria  = ?




Answer

Henoch–Schönlein purpura (HSP)













 HSP  represents with
 palpable purpura,
 diffuse abdominal pain, 
arthritis,
 arthralgia,
 hematuria, 
and/or proteinuria.

HSP can also represent as glomerulonephritis.
HSP glomerulonephritis is characterized by immunoglobulin A (IgA) deposition


 HSP usually precedes an infection, such as a throat infection.

HSP is a systemic vasculitis (inflammation of blood vessels) and is characterized by deposition of immune complexes containing the antibody immunoglobulin A (IgA).

Treatment

symptom control

resolves on its own